A Bump on the Head - An Unusual Presentation of Extraosseus Ewing Sarcoma in a 3-month-old Male
A Bump on the Head - An Unusual Presentation of Extraosseus Ewing Sarcoma in a 3-month-old Male
T Dao MD†, T Beydoun DO†, P Cornejo MD†, S Taylor PA‡, D Carpentieri MD‡, M Patel MD†
Department of Medical Imaging†, Department of Pathology‡
Phoenix Children's Hospital
Phoenix, Arizona, USA
Abstract:
Extraosseus Ewing sarcoma arising in the head and neck is extremely rare, and even more rare in the neonatal period. We present a case of extraosseus Ewing sarcoma involving the right eyelid in a 3-month-old male with a progressively enlarging mass involving the right forehead that was present since 2 weeks of age. The mass was initially thought to be a hemangioma and treated as such, but did not respond to propranolol and steroid treatment. Excisional biopsy was performed and pathology demonstrated Ewing sarcoma. Extraosseus Ewing sarcoma is a rare entity in the neonatal population and should be included in the differential diagnosis of head and neck soft tissue masses despite patient age.
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